Nursing Care of a Child with MOPD II and Moyamoya according to Orem's Self - Care Defifiency Theory: A case Report

Microcephalic osteodysplastic primitive dwarfism (MOPDII) is the most familiar form of microcephalic primordial dwarfism (MPD). The classic features of the MPD group are marked microcephaly and severe antenatal and postnatal growth retardation. Such patients also have the Moyamoya disease, which includes recurrent stroke attacks and possible neurological complications. Today, it is possible to provide care for such patients with many theories. Caring for the children with growth-developmental retardation with Orem's Self-Care Deficiency Theory may enable them to become self-aware and increase their quality of life. The importance of nursing care in this rare disease is undeniable. In this study, the nursing care of a patient with a diagnosis of MOPD2 and Moyamoya was carried out based on the Self-Care Deficit Nursing Theory. "Partly remedial nursing care" was provided as the patient can self-care at a moderate level, and also "supportive and educational nursing care" was provided to support the mother and other family members who provide care to the patient.